Bean Syndrome (blue rubber bleb nevus syndrome)

Aleksandra Gawlikowska-Sroka, Barbara Glura, Małgorzata Mokrzycka, Tomasz Ociepa

Abstract


The blue rubber bleb nevus syndrome or Bean syndrome is a rare disorder characterised by the presence of haemangiomas in the skin and gastrointestinal tract. These lesions are usually accompanied by chronic hypochromic anaemia resulting from gastrointestinal bleeding. The cause of this syndrome is unknown. It mostly occurs as sporadic, but autosomal dominant inheritance has also been described. The diagnosis is based on endoscopy, magnetic resonance imaging and computer tomography. Treatment is usually symptomatic.

Keywords


blue rubber bleb nevus syndrome; Bean syndrome; haemangiomas; anaemia

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References


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DOI: https://doi.org/10.21164/pomjlifesci.138

Copyright (c) 2016 Aleksandra Gawlikowska-Sroka, Barbara Glura, Małgorzata Mokrzycka, Tomasz Ociepa

License URL: https://creativecommons.org/licenses/by-nc-nd/3.0/pl/