THROMBOTIC THROMBOCYTOPENIC PURPURA IN A PATIENT WITH SYSTEMIC LUPUS ERYTHEMATOSUS – COMPLICATION OF CONNECTIVE TISSUE DISEASE OR OVERLAP SYNDROME?

Authors

  • Dominika Grzegowska Katedra i Klinika Chorób Wewnętrznych, Chorób Tkanki Łącznej i Geriatrii Gdańskiego Uniwersytetu Medycznego
  • Anna Masiak Katedra i Klinika Chorób Wewnętrznych, Chorób Tkanki Łącznej i Geriatrii Gdańskiego Uniwersytetu Medycznego
  • Zenobia Czuszyńska Katedra i Klinika Chorób Wewnętrznych, Chorób Tkanki Łącznej i Geriatrii Gdańskiego Uniwersytetu Medycznego
  • Marcin Ziętkiewicz Katedra i Klinika Chorób Wewnętrznych, Chorób Tkanki Łącznej i Geriatrii Gdańskiego Uniwersytetu Medycznego
  • Wojciech Homenda Oddział Chorób Wewnętrznych i Hematologiczny Wojewódzkiego Szpitala Specjalistycznego w Słupsku
  • Michalina Pejska Oddział Chorób Wewnętrznych i Hematologiczny Wojewódzkiego Szpitala Specjalistycznego w Słupsku
  • Zbigniew Zdrojewski Katedra i Klinika Chorób Wewnętrznych, Chorób Tkanki Łącznej i Geriatrii Gdańskiego Uniwersytetu Medycznego

DOI:

https://doi.org/10.21164/pomjlifesci.73

Keywords:

thrombotic thrombocytopenic purpura, systemic lupus erythematosus, metalloproteinase ADAMTS13, thrombotic microangiopathy, overlap syndrome, plasma exchange (PEX)

Abstract

Thrombotic thrombocytopenic purpura (TTP) and systemic lupus erythematosus (SLE) are two separate diseases, whose clinical symptoms may be similar. The coexistence of these two diseases is very rare. We present the case report of a 29-year-old female patient with simultaneous diagnosis of TTP and SLE. The purpose of this article is to draw attention to the diagnostic difficulties which may result from the co-existence of both diseases.

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Published

2016-07-20

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